TY - JOUR T1 - 原发性纤毛运动障碍：诊断和护理JF的标准 - 欧洲呼吸杂志JO - EUR呼吸杂志SP - 982 LP - 988 VL - 12 - 4 AU - 布什，A AU - 科尔，P AU - 哈里里中号AU - 麦凯，我AU - 菲利普斯，G AU - 的O'Callaghan，C AU - 威尔逊，R AU - 华纳，JO Y1 - 1998年10月1日UR - //www.qdcxjkg.com/content/12/4/982.abstract N2 - 原发性纤毛运动障碍（PCD）的特征在于，所述上的疾病和下呼吸道，与内脏镜像排列在相关联的情况下50％，由于不正常的结构和/或纤毛的功能。本文的目的是审查PCD的临床特征，诊断和管理。演示包括新生儿呼吸窘迫，反复下呼吸道感染，慢性鼻窦炎和男性不育。PCD进入支气管扩张，非典型哮喘和异常严重上气道疾病的鉴别诊断。诊断是调查的级联，从患者小于10岁的年龄较大的糖精试验;纤毛运动频率和光镜图案;和电子显微镜来评估睫状形态和取向。这不是混淆原发性和继发性纤毛异常是很重要的。 Nasal nitric oxide is low in PCD, and this measurement shows promise as a screening test for PCD. Diagnosis is important, in order to prevent the development of bronchiectasis and to avoid any unnecessary otorhinolaryngological procedures. Regular follow-up is essential, and management should be multidisciplinary, with input from centres with a special interest in PCD, having access to paediatric and adult chest physicians, otolaryngologists and audiological physicians, physiotherapists, counselling services and fertility clinics. The prognosis is good, but morbidity can be considerable if PCD is incorrectly managed. ER -